1 Introduction Paragangliomas (PGLs), neuroendocrine tumors arising from sympathetic and parasympathetic ganglia, present in the head and neck up to 70% of the time [1]. The most common of these are carotid body tumors (CBT), though other frequent presentations include jugular paraganglioma (JP), glomus tympanicum (GT) (middle ear paragangliomas), and vagal paragangliomas (VP) [2]. PGLs can be caused by mutations in various genes known to be associated with these tumors.
