Friedreich ataxia (FRDA) is a progressive, multisystem, autosomal recessive condition.1 Typical neurological signs include gait and limb truncal ataxia, sensory, and speech disturbances, which arise as a consequence of progressive cell death in the spinal cord and cerebellum.2, 3 Key neuropathological changes in FRDA occur in the dentate nuclei and cerebellar peduncles, dorsal root ganglia, dorsal spinocerebellar tracts, and areas of the brainstem corresponding to the spinocerebellar and...