Case presentation A 6-year-old Nepali patient presented to the Nephrology Clinic at our institution with HTN noted at multiple office visits. He was known to have NF1, with multiple café-au-lait spots, an optic glioma, and a low-grade brain glioma. Blood pressure (BP) readings at their office appointments prior to presentation ranged from 139–154 mmHg to 92–105 mmHg. His family history was significant for maternal HTN, diagnosed at age 36 years old, and a sibling with NF1.