Our patient presented to our institution with a rare, symptomatic, retroperitoneal, unicentric HV-CD tumor. Although etiologic factors continue to be elucidated [7], a major clinical challenge rests first on establishing the diagnosis of CD. An important initial step is a high clinical index of suspicion for CD in symptomatic patients [2]. Regardless of whether it presents as an incidental finding or a symptomatic mass, CD is rarely included within differential diagnoses.
