1 Introduction Inflammatory myofibroblastic tumor (IMT) is a rare mesenchymal neoplasm composed of spindle-shaped myofibroblastic cells and a variable inflammatory infiltrate. Initially identified in the lungs, IMTs have been reported in multiple extrapulmonary sites, including the abdomen and pelvis. Gallbladder involvement, however, is exceedingly rare, with fewer than ten reported cases to date [1, 2]. The etiology of IMT remains unclear but may involve autoimmune or infectious triggers.