Key points Initial diagnosis is achieved via analysis of metanephrine levels followed by CT or MRI.Half of phaeochromocytomas are diagnosed incidentally on abdominal imaging.A greater proportion of phaeochromocytomas are malignant, extra-adrenal, and/or familial than previously suspected.Associated cardiomyopathies occur relatively frequently.Vasopressin is effective in treating catecholamine-resistant hypotension after tumour resection.ClassificationPhaeochromocytomas are...