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Insuficiencia suprarrenal primaria: casuística de cinco hospitales terciarios
Introducción La insuficiencia suprarrenal primaria (ISP) consiste en la incapacidad de las propias glándulas suprarrenales de producir hormonas adrenocorticales (glucorticoides y mineralocorticoides). Se trata de una entidad poco frecuente, situándose la prevalencia en 82 a 144 casos por millón de habitantes y la incidencia en 4 a 6 casos por millón de habitantes, con un predominio hacia el sexo femenino1-3, siendo desconocida su incidencia en la infancia.
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