Niroshan Dayalan

HLH in adults is characterized by fever, cytopenias, hepatosplenomegaly and hyperferritinemia, and carries a high mortality rate [1, 2]. It can occur secondary to infections, autoimmune diseases or malignancies, most commonly of haematological origin [1, 2]. Early identification of the underlying trigger is critical, but the sepsis-like presentation often delays diagnosis and worsens outcomes [3].